ABSTRACT
There is still much to learn about biliary atresia (BA); why it
happens and how it happens being good examples of areas
where there is too much speculation and not enough hard
evidence. What is only too obvious is that if it is untreated it
progresses to end-stage cirrhosis and is potentially fatal
within the first 1218 months. A treatment strategy has evolved, which in the best hands will give a 90% chance of
long-term survival for all infants born with the disease, but,
even in these survivors there is still significant morbidity and
problems to overcome. Nonetheless, it is compatible with
normal life.
