ABSTRACT

Omphalocele (also known as exomphalos) consists of a

central abdominal wall defect that permits herniation of

abdominal viscera into the umbilical cord. A membrane that

is made of Wharton’s jelly, from which the umbilical cord

emerges (Fig. 71.1), covers the viscera. Pare provided the first

description of an omphalocele in 1634. Hey reported the

successful treatment of an omphalocele by primary repair in

1803, and Ahlfeld described the escharotic treatment using

alcohol in 1899. In 1814, Scarpa observed that omphaloceles

were often associated with other congenital anomalies.