ABSTRACT
This chapter presents a case study of a 16-year-old boy. A 16-year-old boy with scarring over his face is referred to the dermatology out-patient clinic. He reports a history of burning and stinging of his skin whilst outside playing football. His parents had also noted his skin would then turn red and blister. Consequently, as a young child they tried to keep him out of the sun as much as possible. Over his cheeks and nose the skin appears waxy and atrophic with multiple areas of pitted scarring. Patients usually report symptoms starting in early childhood. Photosensitivity may be severe with almost immediate stinging, burning and itching following sun exposure. Erythema, oedema, vesicles and purpura appear within 1–8 hours predominantly over the nose, cheeks and dorsi of the hands. Patients should avoid any unnecessary exposure to sunlight and should wear photoprotective clothing / wide-brimmed hat.
