ABSTRACT

Osteochondromata can interfere with normal linear growth of long bones. In the upper limb, deformities of wrist, forearm and elbow may develop in children with hereditary multiple osteochondromatosis.1-5 The pattern of deformities is determined by the location of the osteochondroma5 (Table 20.1). Among the different deformities that may develop, varus deformity of the wrist is common; valgus deformity is less frequently seen. The primary cause of varus deformity of

the wrist is disproportionate shortening of the ulna as a result of growth arrest due to an osteochondroma situated on the distal ulna. The short ulna, in turn, causes compensatory deformities of the less severely affected radius. These secondary radial deformities include diaphyseal bowing and ulnar deviation of the distal articular surface. In addition, the radial head may dislocate. While the wrist deformity may be the most obvious, the abnormalities of the entire limb including the forearm, elbow and wrist need to be addressed if the appearance and function of the limb are to improve.