ABSTRACT
Churg-Strauss syndrome (CSS) was first described in 1951 (1) from an autopsy series of patients thought to have been affected by polyarteritis nodosa (PAN). The main characterisitics of the disease were the presence of asthma, eosinophilia, and histopathological manifestations comprising vasculitis of small-sized vessels, arterioles, and venules associated with granuloma. ChurgStrauss syndrome is now considered to be a well-defined vasculitis, clearly distinct from other small-and/or medium-sized-vessel vasculitides. In this chapter, we review the clinical aspects, outcome, and treatment of CSS.
