ABSTRACT

Aplasia cutis congenita (ACC) is the congenital absence of skin. The scalp is by far the most common site for solitary lesions of ACC. Occasionally two or even three lesions of ACC can occur together on the scalp. Lesions are often located near the hair whorl on the vertex of the scalp, and can be various shapes and sizes (0.5-10 cm). At the time of birth the defects may be deeply ulcerated, superficially eroded or completely healed but scarred (Figure 27.1).