ABSTRACT
Craniofacial microsomia, or otomandibular dyostosis, is a spectrum of soft and hard tissue
hypoplasia typically affecting the regions of Tessier’s #6, #7, and #8 facial clefts (1). It is a disorder
of the first and second branchial arches with an incidence as high as 1 in 3500 live births. The
classic presentation is unilateral mandibular hypoplasia, deficient soft tissues of the face and
microtia. Gorlin’s term, hemifacial microsomia, emphasizes that the disorder is usually a
unilateral facial deformity (70-95% of the time) and should not be confused with Treacher
Collins Syndrome (also aTessier’s #6, #7, and#8 facial clefts),which isbilateral andsymmetric (2).
VARIATION
